Introduction to Retroperitoneal Lymphangioma

What is/are Retroperitoneal Lymphangioma?

Retroperitoneal Lymphangioma - Retroperitoneal lymphangiomas (RL) are rare benign cystic tumors of the lymphatic system, which account for 1% of all lymphangiomas, and till now less than 200 cases have been reported. ^[1] Retroperitoneal lymphangioma is an uncommon and benign mesodermal tumour that arises from the retroperitoneal lymphatics. ^[2] Retroperitoneal lymphangiomas are uncommon lymphatic malformations that present as cystic masses, arise from isolated lymphatic vessels, and do not communicate with the normal lymphatic system. ^[3] Most common presentation of cystic lymphangiomas are in the neck (75%) and axillary region (20%) and only 5% are intra-abdominal, while retroperitoneal lymphangiomas account for only 1% of cases (2). ^[4] Retroperitoneal lymphangiomas occurs due to malformations of retroperitoneal lymphatic systems are extremely rare condition affecting adult patients. ^[5] Objective To explore the clinical characteristics, diagnosis and treatment strategies of neonatal retroperitoneal lymphangioma. ^[6] Retroperitoneal lymphangiomatosis (RL) is a rare form of primary lymphedema featuring aberrant retroperitoneal lymphatic proliferation. ^[7] CECT (Contrast Enhanced Computed Tomography) abdomen suggested the possibility of giant mucocele of appendix and other cystic lesions such as retroperitoneal lymphangioma. ^[8]